Chapter 26: Congenital Heart Disease

CHD anatomy and imaging techniques are explored, with emphasis on pre- and post-interventional TEE. Animated diagrams and congenital videos will support comprehension.

1

Figures

ASD and RV dilatation. (A,B) ME 4C RV focused view with CFI shows dilatation of the RV and RA compared with the left-sided chambers during diastole. CFI shows left-to-right flow through the IAS from a secundum ASD. (C,D) CT scan view of an ASD. Note the IAS gap and the contrast entering the RA from the SVC (arrow at white zone) in a bi-atrial view..<em> Abbreviations</em>: 4C, four-chamber; ASD, atrial septal defect; CFI, color flow imaging; CT, computed tomography; IAS, interatrial septum; LA, left atrium; LV, left ventricle; ME; mid-esophageal; MPA, main pulmonary artery; RA, right atrium; RV, right ventricle; SVC, superior vena cava.<i class='fa fa-video-camera' aria-hidden='true'></i>

eFigure 26.2

ASD and RV dilatation. (A,B) ME 4C RV focused view with CFI shows dilatation of the RV and RA compared with the left-sided chambers during diastole. CFI shows left-to-right flow through the IAS from a secundum ASD. (C,D) CT scan view of an ASD. Note the IAS gap and the contrast entering the RA from the SVC (arrow at white zone) in a bi-atrial view.. Abbreviations: 4C, four-chamber; ASD, atrial septal defect; CFI, color flow imaging; CT, computed tomography; IAS, interatrial septum; LA, left atrium; LV, left ventricle; ME; mid-esophageal; MPA, main pulmonary artery; RA, right atrium; RV, right ventricle; SVC, superior vena cava.

Trabecular or muscular VSD. (A,B) ME color-compare 4C view with CFI shows a trabecular muscular VSD with left-to-right shunt confirmed by the (C) intraoperative findings. (D) The diagram illustrates blood flow related to the VSD shunt.<em> Abbreviations</em>: LA, left atrium; LV, left ventricle; ME, mid-esophageal; RA, right atrium; RV, right ventricle; VSD, ventricular septal defect. <i class='fa fa-video-camera' aria-hidden='true'></i>

eFigure 26.18

Trabecular or muscular VSD. (A,B) ME color-compare 4C view with CFI shows a trabecular muscular VSD with left-to-right shunt confirmed by the (C) intraoperative findings. (D) The diagram illustrates blood flow related to the VSD shunt. Abbreviations: LA, left atrium; LV, left ventricle; ME, mid-esophageal; RA, right atrium; RV, right ventricle; VSD, ventricular septal defect.

31 Congenital MV abnormalities. (A,B) Double-orifice MV in these LA and cut-away atrioventricular diagrams, the smaller of the two orifices is in the right lateral position with variable stenosis. (C) Parachute MV in this cut-away atrioventricular diagram of a stenotic parachute MV demonstrates a single papillary muscle, often the postero-medial, or fused papillary muscles that usually arise from the inferior left ventricular wall.<em> Abbreviations</em>: LA, left atrial; MV, mitral valve. Adapted from Zias et al.<strong><sup>40</sup></strong>

eFigure 26.31

31 Congenital MV abnormalities. (A,B) Double-orifice MV in these LA and cut-away atrioventricular diagrams, the smaller of the two orifices is in the right lateral position with variable stenosis. (C) Parachute MV in this cut-away atrioventricular diagram of a stenotic parachute MV demonstrates a single papillary muscle, often the postero-medial, or fused papillary muscles that usually arise from the inferior left ventricular wall. Abbreviations: LA, left atrial; MV, mitral valve. Adapted from Zias et al.40

2

Videos

Chapter 26 Fig02

Chapter 26 Fig04A

Chapter 26 Fig04E

Chapter 26 Fig05A

Chapter 26 Fig05C

Chapter 26 Fig05D

Chapter 26 Fig05F

Chapter 26 Fig06A

Chapter 26 Fig07A

Chapter 26 Fig08A

Chapter 26 Fig08D

Chapter 26 Fig08E

Chapter 26 Fig09A

Chapter 26 Fig10A

Chapter 26 Fig10C

Chapter 26 Fig11C

Chapter 26 Fig14A

Chapter 26 Fig14B

Chapter 26 Fig15A

Chapter 26 Fig16A

Chapter 26 Fig16B

Chapter 26 Fig16E

Chapter 26 Fig17A

Chapter 26 Fig17C

Chapter 26 Fig17E

Chapter 26 Fig18A

Chapter 26 Fig18C

Chapter 26 Fig19A

Chapter 26 Fig19D

Chapter 26 Fig21A

Chapter 26 Fig21C

Chapter 26 Fig22A

Chapter 26 Fig22C

Chapter 26 Fig22E

Chapter 26 Fig23A

Chapter 26 Fig24A

Chapter 26 Fig24B

Chapter 26 Fig24D

Chapter 26 Fig24F

Chapter 26 Fig25A

Chapter 26 Fig25B

Chapter 26 Fig25D

Chapter 26 Fig26A

Chapter 26 Fig26D

Chapter 26 Fig26G

Chapter 26 Fig27A

Chapter 26 Fig27C

Chapter 26 Fig27E

Chapter 26 Fig27F

Chapter 26 Fig28A

Chapter 26 Fig28B

Chapter 26 Fig28D

Chapter 26 Fig29A

Chapter 26 Fig29B

Chapter 26 Fig29D

Chapter 26 Fig30C

Chapter 26 Fig30E

Chapter 26 Fig30F

Chapter 26 Fig32A

Chapter 26 Fig32C

Chapter 26 Fig32E

Chapter 26 Fig32G

Chapter 26 Fig33AB

Chapter 26 Fig33FG

Chapter 26 Fig35D

Chapter 26 Fig36B

Chapter 26 Fig36C

Chapter 26 Fig36D

Chapter 26 Fig36E

Chapter 26 Fig37A

Chapter 26 Fig37D

Chapter 26 Fig37G

Chapter 26 Fig38A

Chapter 26 Fig38D

Chapter 26 Fig39A

Chapter 26 Fig39C

Chapter 26 Fig40A

Chapter 26 Fig40D

Chapter 26 Fig41A

Chapter 26 Fig42A

Chapter 26 Fig42C

Chapter 26 Fig42E

Chapter 26 Fig43A

Chapter 26 Fig45A

Chapter 26 Fig45D

Chapter 26 Fig46A

Chapter 26 Fig46D

Chapter 26 Fig47A

Chapter 26 Fig47D

3

Tables

eTable 26.2 Recommended TEE views to image congenital cardiac malformations

MalformationViews
Atrial septal defect (Figure 26.3)ME 4C (0°-20°); ME AoV SAX (30°-60°); ME Bicaval (80°-110°)
Ventricular septal defect (Figure 26.13)  ME 4C (0°-20°); ME AoV SAX (30°-60°); ME AoV LAX (120°-160°); TG SAX (0°-30°)
Patent ductus arteriosus (Figure 26.23)UE aortic short axis (90°); TG RV outflow (60°-90°)
AV canal defect or AVSD (Figure 26.20)  ME 4C (0°–20°); AoV LAX (120°–160°); TG basal SAX (0°–20°); TG LAX (90°–110°)
Ebstein’s anomaly (Figure 26.24)  ME 4C (0°–20°); ME RV outflow (60°–90°); TG LAX view of TV (60°–90°)
Pulmonary stenosis (See Figure 19.12)UE RV outflow (60°–90°); TG RV outflow (60°–90°)
Tetralogy of Fallot (Figure 26.26)  ME 4C (0°–20°); ME AoV SAX (30°–60°); ME AoV LAX (120°–160°); TG RV outflow (60°–90°)
Cor triatriatum (Figure 26.30)ME 4C (0°–20°); ME 2C (80°–100°)
Mitral valve stenosis (eFigure 26.31)  ME 4C (0°–20°); ME 2C (80°–100°); ME LAX (80°–100°); TG basal SAX (0°–25°); TG LAX (120°–160°)
Cleft mitral valve (Figure 26.22)ME 4C (0°–20°); ME 2C (80°–100°); TG basal SAX (0°–20°)
Aortic valve stenosis (See Figure 14.31)  ME AoV SAX (30°–60°), ME AoV LAX (120°–160°); ME ascending aorta LAX (90°); TG LAX (90°–120°); DTG (0°–30°)
Subvalvular AS (See Figure 14.20)ME 5C (0°–20°); TG LAX (90°–120°)
Supravalvular AS (See Figure 14.19)  ME AoV LAX (120°–160°); ME ascending aorta LAX (90°); DTG (0°–30°)
Coarctation of aorta (See Figure 23.45.)UE aortic arch LAX (0°); UE aortic arch SAX (90°)
Truncus arteriosus (Figure 26.14)  ME 4C (0°–20°); ME AoV SAX (30°–60°); ME AoV LAX (120°–160°); TG RV outflow (60°–90°)
Transposition of the great arteries (Figure 26.34)  ME 4C (0°–20°); ME Bicaval (80°–110°); ME AoV SAX (30°–60°); ME AoV LAX (120°–160°); TG basal SAX (0°–20°); TG mid SAX (0°–20°) 
Complex single ventricle (Figure 26.42)  ME 4C (0°–20°); ME Bicaval (80°–110°); ME AoV SAX (30°–60°); ME AoV LAX (120°–160°) TG RV outflow (60°–90°); TG basal SAX (0°–20°); TG Mid SAX (0°–20°) 
Abbreviations: 2C, two-chamber; 4C, four chamber; 5C, five-chamber; AoV, aortic valve; AS, aortic stenosis; AVSD, endocardial cushion defect; DTG, deep transgastric; LAX. Long-axis; ME, mid-esophageal; RV, right ventricular; SAX, short-axis; SD, septal defect; TEE, transesophageal echocardiography; TG, transgastric; TV, tricuspid valve; UE, upper esophageal.